Interstitial lung disease codes

Codelist metadata

Coding system

SNOMED CT

Coding system release

39.2.0

Organisation

NHSD Primary Care Domain Refsets

Codelist ID

nhsd-primary-care-domain-refsets/interstitial-lung-disease-codes

Version Tag

20241205

Version ID

40949454

Versions

About

Description

Taken from the ILD_COD refset published by NHSD.


Codelists are developed by a broad community of users for individual study purposes, which may or may not meet the needs of other studies. They should not be thought of as universal definitions of a particular condition.

We don't offer any guarantees about what they do or don't identify. Users should carefully check that any codelist meets their needs, and seek clinical input where appropriate.

code term
1017196003 Interstitial pulmonary fibrosis due to inhalation of substance
1017197007 Interstitial pulmonary fibrosis due to inhalation of drug
10713006 Diffuse interstitial rheumatoid disease of lung
111280008 Rheumatoid pneumoconiosis
1163147006 Chronic fibrosis of lung caused by Aspergillus
1172606002 Idiopathic pleuroparenchymal fibroelastosis
1177007001 Fibrosis of lung due to pulmonary paracoccidioidomycosis
1177120001 Bronchiolitis obliterans syndrome due to and following allogeneic stem cell transplant
1222677008 Interstitial lung disease due to surfactant protein C deficiency
1222678003 Interstitial lung disease due to ATP-binding cassette subfamily A member 3 deficiency
1222679006 Autoimmune interstitial lung disease, arthritis syndrome
1228876007 Severe early-onset pulmonary alveolar proteinosis due to methionyl-transfer ribonucleic acid synthetase 1 deficiency
123592004 Acute mucous pneumonia
1259003 Schistosis
1284850005 Interstitial lung disease due to and following radiotherapy
129451001 Respiratory bronchiolitis associated interstitial lung disease
129452008 Nonspecific interstitial pneumonitis
129458007 Bronchiolitis obliterans organizing pneumonia
129459004 Acute interstitial pneumonia
13274008 Atrophic fibrosis of lung
14700006 Bauxite fibrosis of lung
155554001 Mycoplasmal pneumonia
155587002 Pneumoconiosis
155588007 Coal workers' pneumoconiosis
155600007 Radiation-induced diffuse interstitial pulmonary fibrosis
155613001 Pulmonary fibrosis
155624004 Idiopath. fibrosing alveolitis (& Hamman-Rich syndrome)
17385007 Graphite fibrosis of lung
17996008 Pneumoconiosis caused by inorganic dust
18121009 Chronic berylliosis
18354001 Chronic induration of lung
186726005 Human immunodeficiency virus disease resulting in lymphoid interstitial pneumonitis
187233002 Sarcoidosis of lung with sarcoidosis of lymph nodes
192658007 Giant cell interstitial pneumonitis
192681000000108 Cryptogenic organising pneumonitis
195894001 Mycoplasmal pneumonia
195895000 Mycoplasmal pneumonia
195896004 Pneumonia caused by pleuropneumonia-like organism
196006003 Asbestosis NOS
196009005 Massive silicotic fibrosis
196010000 Silica pneumoconiosis NOS
196011001 Pneumoconiosis due to other inorganic dust
196012008 Pneumoconiosis due to inorganic dust NOS
196016006 Pneumoconiosis NOS
196017002 Pneumoconiosis associated with tuberculosis
196027008 Toxic bronchiolitis obliterans
196028003 Chronic pulmonary fibrosis caused by chemical fumes
196044007 Complicated pneumoconiosis
196049002 Chronic pulmonary radiation disease
196051003 Drug-induced interstitial lung disorder
196053000 Chronic drug-induced interstitial lung disorders
196121006 Lung: [cirrhosis of] or [postinflammatory pulmonary fibrosis]
196122004 Other alveolar and parietoalveolar disease
196123009 Fibrosing alveolitis: [idiopathic] or [cryptogenic]) or (Hamman - Rich syndrome)
196125002 Diffuse interstitial pulmonary fibrosis
196126001 Idiopathic fibrosing alveolitis NOS
196129008 Other alveolar and parietoalveolar disease NOS
196130003 Alveolar and parietoalveolar disease NOS
196133001 Lung disease with systemic sclerosis
196135008 Pulmonary amyloidosis
196137000 Lung disease with Sjögren's disease
196161007 Interstitial lung disease NEC
196233007 [X]Pneumoconiosis due to other dust containing silica
196234001 [X]Pneumoconiosis due to other specified inorganic dusts
196245003 [X]Other respiratory diseases principally affecting the interstitium
196246002 [X]Other interstitial pulmonary diseases with fibrosis
196247006 [X]Other specified interstitial pulmonary diseases
206300003 Other specified perinatal interstitial emphysema or related condition
206313009 Prematurity with interstitial pulmonary fibrosis
22607003 Asbestosis
233621003 Rickettsial pneumonia
233623000 Mononuclear interstitial pneumonitis
233673002 Drug-induced bronchiolitis obliterans
233692000 Cryptogenic pulmonary eosinophilia
233703007 Interstitial lung disease
233713004 Seasonal cryptogenic organizing pneumonia with biochemical cholestasis
233714005 Diffuse infiltrative lung disease
233717003 Diffuse pulmonary neurofibromatosis
233718008 Pulmonary tuberous sclerosis
233721005 Usual interstitial pneumonitis
233723008 Bronchiolitis obliterans with usual interstitial pneumonitis
233724002 Toxic diffuse interstitial pulmonary fibrosis
233725001 Drug-induced diffuse interstitial pulmonary fibrosis
233726000 Localized pulmonary fibrosis
233738009 Fibrous mediastinitis caused by radiation
233748006 Simple pneumoconiosis
233749003 Complicated pneumoconiosis
233750003 Erionite pneumoconiosis
233751004 Metal pneumoconiosis
233754007 Cerium pneumoconiosis
233755008 Nickel pneumoconiosis
233756009 Thorium pneumoconiosis
233757000 Zirconium pneumoconiosis
233758005 Mica pneumoconiosis
233759002 Mixed mineral dust pneumoconiosis
233760007 Acute silicosis
233761006 Subacute silicosis
233762004 Chronic silicosis
233763009 Silicotuberculosis
233764003 Wollastonite pneumoconiosis
233767005 Stage 1 pulmonary sarcoidosis
233768000 Stage 2 pulmonary sarcoidosis
233769008 Stage 3 pulmonary sarcoidosis
233770009 Stage 4 pulmonary sarcoidosis
233772001 Sarcoid pulmonary calcification
234161007 Familial pulmonary capillary hemangiomatosis
236302005 Acute interstitial pneumonitis
24369008 Pulmonary sarcoidosis
26511004 Pneumoconiosis caused by sisal fiber
266368002 Post-inflammatory pulmonary fibrosis
266404004 Chronic chemical respiratory disease
266410004 Idiopath. fibrosing alveolitis (& Hamman-Rich syndrome)
276696002 Pulmonary fibroplasia
277844007 Pulmonary lymphangioleiomyomatosis
28168000 Idiopathic fibrosing alveolitis, chronic form
29422001 Coal workers' pneumoconiosis
30042003 Confluent fibrosis of lung
302913000 Diffuse pulmonary calcinosis
32139003 Mixed dust pneumoconiosis
328641000119109 Genetic disorder of surfactant dysfunction
328661000119108 Interstitial lung disease of childhood
33548005 Anthracosilicosis
34004002 Siderosilicosis
35037009 Primary atypical interstitial pneumonia
3514002 Peribronchial fibrosis of lung
361194002 Perinatal pulmonary fibroplasia
361195001 Pulmonary fibroplasia
361196000 Idiopathic hilar fibrosis
36599006 Chronic fibrosis of lung
36696005 Kaolinosis
370658281000119103 Acute respiratory distress syndrome due to dabbing
397981000000105 [X]Other respiratory diseases principally affecting the interstitium
397991000000107 [X]Other interstitial pulmonary diseases with fibrosis
398640008 Rheumatoid arthritis with pneumoconiosis
40122008 Pneumoconiosis
40218008 Carbon electrode makers' pneumoconiosis
40527005 Idiopathic pulmonary hemosiderosis
405570007 Pulmonary fibrosis due to and following radiotherapy
40640008 Massive fibrosis of lung co-occurrent and due to silicosis
419331000000108 [X]Other specified interstitial pulmonary diseases
426437004 Familial idiopathic pulmonary fibrosis
426853005 Pneumoconiosis caused by silicate
427123006 Interstitial lung disease due to collagen vascular disease
432461000000108 [X]Pneumoconiosis due to other dust containing silica
44274007 Lymphoid interstitial pneumonitis
44547005 Chalicosis
451271000000107 [X]Pneumoconiosis due to other specified inorganic dusts
45157009 Idiopathic fibrosing alveolitis
46970008 Pneumonia caused by Mycoplasma pneumoniae
470101491000119107 Interstitial lung disease due to dabbing
47515009 Simple silicosis
47938003 Chronic obliterative bronchiolitis
49840000 Complicated silicosis
50196008 Perialveolar fibrosis of lung
51615001 Fibrosis of lung
535011000000101 Interstitial lung disease NEC
54867000 Rheumatoid arthritis with fibrosing alveolitis
556179491000119104 Interstitial lung disease due to vaping
566831000000101 Other specified perinatal interstitial emphysema or related condition
56841008 Massive fibrosis of lung
57124002 Postinflammatory pulmonary fibrosis
57488007 Chronic pulmonary fibrosis due to inhalation of chemical fumes AND/OR vapors
58691003 Antimony pneumoconiosis
593591000000107 Pneumoconiosis due to inorganic dust NOS
611551000000109 Asbestosis NOS
621081000000104 Alveolar and parietoalveolar disease NOS
62161000000102 Interstitial lung disease annual review
625961000000109 Silica pneumoconiosis NOS
625971000000102 Pneumoconiosis due to other inorganic dust
626071000000107 Pneumoconiosis NOS
64631008 Fullers' earth disease
64667001 Interstitial pneumonia
649161000000106 Other alveolar and parietoalveolar disease
649171000000104 Idiopathic fibrosing alveolitis NOS
649181000000102 Other alveolar and parietoalveolar disease NOS
68409003 Organized pneumonia
684633371000119107 Diffuse pulmonary meningotheliomatosis
68759006 Idiopathic fibrosing alveolitis, subacute form
697912009 Pulmonary hypertension due to interstitial lung disease
697921005 Pulmonary hypertension in sarcoidosis
697923008 Pulmonary hypertension in lymphangioleiomyomatosis
700249006 Idiopathic interstitial pneumonitis
700250006 Idiopathic pulmonary fibrosis
700251005 Chronic idiopathic pulmonary fibrosis
700252003 Subacute idiopathic pulmonary fibrosis
704345008 Chronic interstitial pneumonitis
707433009 Lymphangioleiomyomatosis due to tuberous sclerosis syndrome
707434003 Pulmonary fibrosis due to Hermansky-Pudlak syndrome
707435002 Neuroendocrine cell hyperplasia of infancy
707541006 Acute respiratory distress in newborn with surfactant disorder
707551007 Pulmonary interstitial glycogenosis
708026002 Chronic pneumonitis of infancy
708030004 Pulmonary emphysema co-occurrent with fibrosis of lung
708537005 Acute idiopathic pulmonary fibrosis
711164003 STING-associated vasculopathy with onset in infancy
711379004 Interstitial lung disease due to connective tissue disease
71193007 Fibrosis of lung caused by radiation
713244007 Drug induced pulmonary fibrosis
719218000 Cryptogenic organizing pneumonia
721977007 Lung fibrosis, immunodeficiency, 46,XX gonadal dysgenesis syndrome
72270005 Collagenous pneumoconiosis
723829000 Pulmonary fibrosis, hepatic hyperplasia, bone marrow hypoplasia syndrome
73144008 Pneumoconiosis caused by talc
733453005 Congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome
7343008 Liparitosis
737181009 Interstitial lung disease due to systemic disease
737182002 Interstitial lung disease due to granulomatous disease
737183007 Interstitial lung disease due to metabolic disease
737184001 Interstitial lung disease co-occurrent and due to systemic vasculitis
7548000 Rheumatic pneumonitis
76090006 Pittsburgh pneumonia
76157009 Bituminosis
762618008 Bronchiolitis obliterans syndrome due to and after lung transplantation
770760006 16q24.1 microdeletion syndrome
771306007 Hereditary fibrosing poikiloderma, tendon contractures, myopathy, pulmonary fibrosis syndrome
77690003 Interstitial emphysema of lung
781651000000101 Respiratory bronchiolitis associated interstitial lung disease
781661000000103 Interstitial lung disease due to collagen vascular disease
781711000000106 Interstitial lung disease due to connective tissue disease
783182004 Chronic respiratory distress with surfactant metabolism deficiency
785345002 Pneumoconiosis caused by sisal dust
78723001 Cannabinosis
789574002 Acute exacerbation of idiopathic pulmonary fibrosis
805002 Pneumoconiosis caused by silica
805261000000101 Bronchiolitis obliterans syndrome after lung transplantation
807391000000107 Usual interstitial pneumonitis
807851000000108 Pulmonary fibrosis
807861000000106 Respiratory bronchiolitis associated interstitial lung disease
807871000000104 Interstitial lung disease due to collagen vascular disease
807891000000100 Interstitial lung disease due to connective tissue disease
82939003 Chronic rheumatoid nodular fibrosis
83316006 Pneumoconiosis due to silicates
840350008 Chronic obliterative bronchiolitis caused by chemical fumes
840351007 Chronic obliterative bronchiolitis caused by vapor
846637007 Chronic pulmonary fibrosis caused by chemical vapors
85438006 Diatomaceous earth disease
8549006 Desquamative interstitial pneumonitis
86263001 Cobaltosis
866103007 Interstitial lung disease due to juvenile polymyositis
870573008 Interstitial pneumonitis with autoimmune features
87909002 Hard metal pneumoconiosis
88687001 Manganese pneumonitis
90117007 Tuberculous fibrosis of lung
90610005 Interstitial pulmonary fibrosis of prematurity
90623003 Aluminosis of lung

Codes not in the full codelist are in faint grey.