PRIMIS - Lung-specific fibrosis

Codelist metadata

Coding system
SNOMED CT (UK Clinical Edition)
Coding system release
unknown
Author
Tom Nichols
Codelist ID
user/tom-nichols/primis-lung-specific-fibrosis
Version ID
7962e0a8
Number of codes included
574

Versions

About

No metadata has been provided for this codelist.


Codelists are developed by a broad community of users for individual study purposes, which may or may not meet the needs of other studies. They should not be thought of as universal definitions of a particular condition.

We don't offer any guarantees about what they do or don't identify. Users should carefully check that any codelist meets their needs, and seek clinical input where appropriate.

code term
1010333003 Emphysema of left lung
1010334009 Emphysema of right lung
1010616001 Cirrhosis of liver due to classical cystic fibrosis
1017196003 Interstitial pulmonary fibrosis due to inhalation of substance
1017197007 Interstitial pulmonary fibrosis due to inhalation of drug
10501004 Pulmonary alveolar proteinosis
105978008 Extrinsic allergic respiratory disease
106001000119101 Chronic obstructive lung disease co-occurrent with acute bronchitis
10692761000119107 Asthma-chronic obstructive pulmonary disease overlap syndrome
10713006 Diffuse interstitial rheumatoid disease of lung
10785007 Vinyard sprayers' lung
111280008 Rheumatoid pneumoconiosis
111292008 Necrotizing sarcoid granulomatosis
111936002 Cerebral sarcoidosis
111937006 Sarcoidosis, nodular type
115666004 Animal handlers' lung
1192004 Familial amyloid neuropathy, Finnish type
11944003 Feather-pickers' disease
12088005 Budgerigar-fanciers' disease
1212005 Childhood type dermatomyositis
12181002 Tropical pulmonary alveolitis
1259003 Schistosis
126766000 Lymphoepithelial sialadenitis of Sjögren's syndrome
128460000 Systemic sclerosis, diffuse
128461001 Systemic sclerosis sine scleroderma
129451001 Respiratory bronchiolitis associated interstitial lung disease
129452008 Nonspecific interstitial pneumonia
13151001 Flax-dressers' disease
13274008 Atrophic fibrosis of lung
13394002 Suberosis
135836000 End stage chronic obstructive airways disease
13645005 Chronic obstructive lung disease
140190005 O/E - fibrosis of lung present
14700006 Bauxite fibrosis of lung
15123008 Familial amyloid nephropathy with urticaria AND deafness
154425004 Sarcoidosis
154767009 Cystic fibrosis
154769007 Amyloidosis
155565006 Chronic obstructive lung disease
155569000 Chronic obstructive lung disease
155573002 Emphysema
155581001 (Extrinsic allergic alveolitis) or (farmers' lung) or (pneumonitis, allergic NOS)
155589004 (Asbestosis) or (byssinosis) or (pleural plaque disease)
155600007 Radiation-induced diffuse interstitial pulmonary fibrosis
155613001 Pulmonary fibrosis
155624004 Idiopath. fibrosing alveolitis (& Hamman-Rich syndrome)
156455009 (Sicca - Sjogren's - syndrome) or (keraconjunctivitis sicca) or (Sjogren's disease)
156456005 Dermatomyositis
15708009 Benign pneumoconiosis
16003001 Giant bullous emphysema
162974009 On examination - fibrosis of lung present
16573007 Senile cardiac amyloidosis
16623004 Coffee-workers' lung
16846004 Obstructive emphysema
17363001 Splenic sarcoidosis
17385007 Graphite fibrosis of lung
1751000119100 Acute exacerbation of chronic obstructive airways disease with asthma
17602002 Amyloidosis
17996008 Pneumoconiosis caused by inorganic dust
18690003 Farmers' lung
187230004 Pulmonary sarcoidosis
187232007 Lymph node sarcoidosis
187233002 Sarcoidosis of lung with sarcoidosis of lymph nodes
187235009 Sarcoidosis of inferior turbinates
187236005 Arthritis secondary to sarcoidosis
19076009 Sick building syndrome
190905008 Cystic fibrosis
190906009 Cystic fibrosis with no meconium ileus
190907000 Meconium ileus in cystic fibrosis
190908005 Cystic fibrosis with pulmonary manifestations
190909002 Cystic fibrosis with intestinal manifestations
190910007 Cystic fibrosis with other manifestations
190911006 Cystic fibrosis NOS
190923000 Sporadic primary amyloidosis
190929001 [X]Heredofamilial amyloidosis, unspecified
190931005 Amyloidosis NOS
191033003 [X]Sarcoidosis of other and combined sites
191121005 [X]Heredofamilial amyloidosis, unspecified
192658007 Giant cell interstitial pneumonitis
192673008 Sarcoid meningitis
19274004 Grain-handlers' disease
193101001 Multiple cranial nerve palsies in sarcoidosis
193195000 Sarcoid neuropathy
193247000 Amyloid myopathy
193251003 Sarcoid myopathy
193253000 Myopathy due to Sjögren's disease
195033009 Sarcoid heart muscle disease
195896004 Pneumonia caused by pleuropneumonia-like organism
195935004 Chronic obstructive lung disease
195948000 Chronic obstructive lung disease
195950008 Emphysematous bronchitis
195951007 Acute exacerbation of chronic obstructive airways disease
195957006 Chronic bullous emphysema
195958001 Segmental bullous emphysema
195959009 Zonal bullous emphysema
195960004 (Bullous emphysema with collapse) or (tension pneumatocoele)
195961000 Chronic bullous emphysema NOS
195963002 Acute vesicular emphysema
195964008 Emphysema: [acute interstitial] or [atrophic - senile]
195965009 (Sawyer-Jones syndrome) or (other emphysema NOS)
195989002 Pituitary snuff-takers' disease
196001008 Chronic obstructive pulmonary disease with acute lower respiratory infection
196004000 Lung disease: [pneumoconioses] or [occupational] or [due to external agents]
196005004 Asbestos-induced pleural plaque
196006003 Asbestosis NOS
196017002 Pneumoconiosis associated with tuberculosis
196026004 Chronic emphysema caused by chemical fumes
196028003 Chronic pulmonary fibrosis caused by chemical fumes
196051003 Drug-induced interstitial lung disorder
196052005 Acute drug-induced interstitial lung disorder
196053000 Chronic drug-induced interstitial lung disorders
196115007 Pulmonary congestion and hypostasis
196116008 Pulmonary hypostasis
196121006 Lung: [cirrhosis of] or [postinflammatory pulmonary fibrosis]
196123009 Fibrosing alveolitis: [idiopathic] or [cryptogenic]) or (Hamman - Rich syndrome)
196125002 Diffuse interstitial pulmonary fibrosis
196126001 Idiopathic fibrosing alveolitis NOS
196133001 Lung disease with systemic sclerosis
196135008 Pulmonary amyloidosis
196137000 Lung disease with Sjögren's disease
196151000 Pulmonary insufficiency following shock
196152007 Pulmonary insufficiency following surgery
196153002 Pulmonary insufficiency following trauma
196161007 Interstitial lung disease NEC
197368002 Hepatic granulomas in sarcoidosis
199524005 Fetus with chromosomal abnormality (& suspect: [CF] or [mongol])
201443009 Systemic sclerosis induced by drugs and chemicals
201444003 (Sicca - Sjogren's - syndrome) or (keratoconjunctivitis sicca)
201445002 Dermatomyositis (& [Poikilodermatomyositis])
201446001 Juvenile dermatomyositis
201447005 Dermatomyositis with malignant disease
201813004 (Rheumatoid lung) or (Caplan's syndrome) or (fibrosing alveolitis associated with rheumatoid arthritis)
203042003 Myositis in sarcoidosis
203785004 [X]Other dermatomyositis
20606002 Acute bovine pulmonary emphysema AND edema
206303001 Perinatal lung intra-alveolar hemorrhage
206313009 Prematurity with interstitial pulmonary fibrosis
206471004 Perinatal jaundice due to mucoviscidosis
209962000 Myeloma-associated amyloidosis
21787007 Sarcoidosis, Darier-Roussy type
22607003 Asbestosis
230193008 Neurosarcoidosis
23132008 Amyloid light-chain amyloidosis
231799005 Sarcoid skin of eyelid
232368009 Nasal sarcoidosis
232458003 Laryngeal sarcoidosis
23315001 Sequoiosis
233621003 Rickettsial pneumonia
233623000 Mononuclear interstitial pneumonia
233636000 Asbestos pleurisy
233653007 Asbestos-induced pleural fibrosis
233655000 Asbestos-induced bilateral diffuse pleural thickening
233659006 Asbestos-induced pleural plaque
233672007 Byssinosis grade 3
233674008 Pulmonary emphysema in alpha-1 primary immunodeficiency deficiency
233675009 Toxic emphysema
233676005 Congenital lobar emphysema
233677001 Scar emphysema
233694004 Dog house disease
233695003 Dry rot lung
233696002 Lycoperdonosis
233697006 New Guinea lung
233698001 Paprika splitters' lung
233699009 Pyrethrum alveolitis
233700005 Rodent handlers' lung
233701009 Sewage workers' lung
233702002 Summer-type hypersensitivity pneumonitis
233703007 Interstitial lung disease
233713004 Seasonal cryptogenic organizing pneumonia with biochemical cholestasis
233716007 Micronodular pulmonary ossification
233717003 Diffuse pulmonary neurofibromatosis
233724002 Toxic diffuse interstitial pulmonary fibrosis
233725001 Drug-induced diffuse interstitial pulmonary fibrosis
233726000 Localized pulmonary fibrosis
233743002 Mediastinal lymph node sarcoidosis
233744008 Hilar lymph node sarcoidosis
233748006 Simple pneumoconiosis
233749003 Complicated pneumoconiosis
233751004 Metal pneumoconiosis
233754007 Cerium pneumoconiosis
233755008 Nickel pneumoconiosis
233756009 Thorium pneumoconiosis
233757000 Zirconium pneumoconiosis
233758005 Mica pneumoconiosis
233759002 Mixed mineral dust pneumoconiosis
233760007 Acute silicosis
233761006 Subacute silicosis
233762004 Chronic silicosis
233763009 Silicotuberculosis
233764003 Wollastonite pneumoconiosis
233767005 Stage 1 pulmonary sarcoidosis
233768000 Stage 2 pulmonary sarcoidosis
233769008 Stage 3 pulmonary sarcoidosis
233770009 Stage 4 pulmonary sarcoidosis
233771008 Endobronchial sarcoidosis
233772001 Sarcoid pulmonary calcification
233774000 Humidifier fever
234523003 Arthritis secondary to sarcoidosis
234524009 Sarcoid dactylitis
234526006 Ocular sarcoidosis
234527002 Lacrimal and parotid gland sarcoidosis
234528007 Nasopharyngeal sarcoidosis
234529004 Acute sarcoid polymyositis
234530009 Chronic sarcoid myopathy
234531008 Orofacial sarcoid
235978006 Cystic fibrosis of pancreas
236302005 Acute interstitial pneumonia
236502006 Renal involvement in scleroderma
236503001 Acute scleroderma renal crisis
237151009 Suspect cystic fibrosis fetus
237864008 AL amyloidosis
237874006 Primary sporadic amyloid myopathy
237877004 Wild type ATTR amyloidosis
238674006 Acute skin sarcoidosis
238675007 Sarcoidosis-induced erythema nodosum
238676008 Lofgrens syndrome
238677004 Maculopapular sarcoidosis
238678009 Chronic skin sarcoidosis
238679001 Sarcoidosis in scar
238680003 Papular sarcoidosis
238681004 Lichenoid sarcoidosis
238935002 Dermatomyositis sine myositis
238936001 Sclerodermatomyositis
23958009 Vanishing lung
239794002 Fibrosing alveolitis associated with rheumatoid arthritis
239901009 Dermatomyositis with malignant disease
239912009 Primary Sjögren's syndrome
239913004 Primary Sjögren's syndrome with organ/system involvement
239914005 Primary Sjögren's syndrome with multisystem involvement
239915006 Secondary Sjögren's syndrome
239916007 Secondary Sjögren's syndrome with organ/system involvement
239917003 Secondary Sjögren's syndrome with multisystem involvement
240629003 Malarial shock lung
24369008 Pulmonary sarcoidosis
25897000 Malt-workers' lung
266355005 Bullous emphysema with collapse
266356006 Atrophic (senile) emphysema
266368002 Post-inflammatory pulmonary fibrosis
266399001 (Extrinsic allergic alveolitis) or (farmers' lung) or (pneumonitis, allergic NOS)
266400008 (Asbestosis) or (byssinosis) or (pleural plaque disease)
266410004 Idiopath. fibrosing alveolitis (& Hamman-Rich syndrome)
268050000 (Sicca - Sjogren's - syndrome) or (keraconjunctivitis sicca) or (Sjogren's disease)
274945004 Amyloid A amyloidosis
277844007 Pulmonary lymphangioleiomyomatosis
28122003 Pulmonary eosinophilic granuloma
281358000 Idiopathic dermatomyositis
28168000 Idiopathic fibrosing alveolitis, chronic form
281882003 AD type amyloidosis
285381006 Acute infective exacerbation of chronic obstructive airways disease
286451000000100 Cystic fibrosis related diabetes mellitus
292571000000107 Cystic fibrosis related diabetes mellitus
293991000000106 Very severe chronic obstructive pulmonary disease
29422001 Coal workers' pneumoconiosis
296241000119107 Disorder of respiratory system due to dermatomyositis
298285004 Systemic sclerosis with limited cutaneous involvement
299276009 Limited systemic sclerosis
30042003 Confluent fibrosis of lung
302401000000105 Suspected cystic fibrosis
302913000 Diffuse pulmonary calcinosis
307732006 Cystic fibrosis with other manifestations
310607007 Sarcoidosis of inferior turbinates
311671000119100 Juvenile dermatomyositis co-occurrent with respiratory involvement
313296004 Mild chronic obstructive pulmonary disease
313297008 Moderate chronic obstructive pulmonary disease
313299006 Severe chronic obstructive pulmonary disease
31541009 Sarcoidosis
31848007 Calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia syndrome
31898008 Paraseptal emphysema
319841000119107 Rheumatoid lung disease with rheumatoid arthritis
320681000119102 Tubulointerstitial nephropathy due to Sjogren syndrome
32139003 Mixed dust pneumoconiosis
328641000119109 Genetic disorder of surfactant dysfunction
328661000119108 Interstitial lung disease of childhood
33325001 Compensatory emphysema
33548005 Anthracosilicosis
34004002 Siderosilicosis
35037009 Primary atypical interstitial pneumonia
35080000 Amyloidosis, type I
3514002 Peribronchial fibrosis of lung
359676009 Congenital lobar emphysema
36042005 Parietoalveolar pneumopathy
361196000 Idiopathic hilar fibrosis
361197009 Sarcoid arthropathy
361198004 Sarcoid arthritis
36599006 Chronic fibrosis of lung
36696005 Kaolinosis
367528006 Amyloidosis due to familial Mediterranean fever
367601000119103 Hereditary amyloidosis
37061001 Granulomatous sarcoid nephropathy
37471005 Extrinsic allergic alveolitis
37711000 Cadmium pneumonitis
38729007 Wheat weevil disease
38826005 Dermatomyositis
39041004 Restrictive cardiomyopathy secondary to sarcoidosis
390898003 Interstitial pulmonary emphysema
39502009 Isolated atrial amyloid
396229003 Adult type dermatomyositis
396230008 Dermatomyositis
398229007 Amyloid polyneuropathy type I
398640008 Rheumatoid pneumoconiosis
398726004 Rheumatoid lung disease
400127001 Sarcoidal granuloma of skin
40122008 Pneumoconiosis
40218008 Carbon electrode makers' pneumoconiosis
402368008 Ichthyosiform sarcoidosis
402369000 Atrophic sarcoidosis
402370004 Ulcerative sarcoidosis
402371000 Verrucous sarcoidosis
402372007 Subcutaneous nodular sarcoidosis
402373002 Hypomelanotic sarcoidosis
402374008 Nail dystrophy due to sarcoidosis
402379003 Talc granuloma of umbilicus
402380000 Sea-urchin granuloma
402425006 Adult onset dermatomyositis
402453006 Amyloid light chain amyloidosis due to multiple myeloma
402454000 Primary systemic amyloidosis due to occult plasma cell dyscrasia
402457007 Secondary systemic amyloidosis affecting skin (AA fibril type)
402459005 Heredofamilial systemic amyloidosis affecting skin
402460000 Familial amyloid polyneuropathy with cutaneous amyloidosis
402712002 Occupational scleroderma
402719006 Systemic amyloidosis affecting skin
403635000 Drug-induced dermatomyositis
404807005 Cheese-washers' lung
40527005 Idiopathic pulmonary hemosiderosis
405570007 Pulmonary fibrosis due to and following radiotherapy
40640008 Massive fibrosis of lung co-occurrent and due to silicosis
413011000000101 [X]Heredofamilial amyloidosis, unspecified
415061000000103 [X]Heredofamilial amyloidosis, unspecified
41590007 Familial amyloid polyneuropathy, Jewish type
41997000 Asthmatic pulmonary alveolitis
42295001 Familial amyloid polyneuropathy
425384007 Sarcoidosis with glomerulonephritis
425879009 Amyloid A nephropathy
426437004 Familial idiopathic pulmonary fibrosis
426598005 Amyloid light-chain nephropathy
426705001 Diabetes mellitus co-occurrent and due to cystic fibrosis
426853005 Pneumoconiosis caused by silicate
427022004 Liver disease due to cystic fibrosis
427089005 Diabetes mellitus due to cystic fibrosis
427123006 Interstitial lung disease due to collagen vascular disease
428301001 Suspected cystic fibrosis
4416007 Heerfordt's syndrome
442012008 Amyloidogenic transthyretin amyloidosis
44274007 Lymphoid interstitial pneumonia
443872005 Systemic sclerosis caused by chemical
444133002 Progressive systemic sclerosis
44547005 Chalicosis
4463009 Familial amyloid polyneuropathy, type II
44833003 Pseudolymphoma of lung in Sjögren's disease
45145000 Unilateral emphysema
45157009 Idiopathic fibrosing alveolitis
452681000000101 [X]Sarcoidosis of other and combined sites
462101000000107 [X]Other dermatomyositis
4645000 Senile brain amyloidosis
46622000 Keratoconjunctivitis sicca, not specified as Sjögren's
46696008 Dilated cardiomyopathy secondary to dermatomyositis
46970008 Pneumonia caused by Mycoplasma pneumoniae
47515009 Simple silicosis
47895001 Congenital emphysema
47938003 Chronic obliterative bronchiolitis
48347002 Humidifier lung
48713002 Amyloid nephropathy
4981000 Panacinar emphysema
49840000 Complicated silicosis
50076003 Baritosis
50196008 Perialveolar fibrosis of lung
50581000 Goodpasture's syndrome
50589003 Silver polishers' lung disease
510351000000103 AL amyloidosis
51277007 Stannosis
5134006 Familial amyloid polyneuropathy, type VI
515611000000104 Cystic fibrosis monitoring
515621000000105 Cystic fibrosis monitoring
515631000000107 Cystic fibrosis annual review
51615001 Fibrosis of lung
52333004 Mushroom workers' lung
526071000000104 Arthropathy in cystic fibrosis
526091000000100 Cystic fibrosis with distal intestinal obstruction syndrome
526101000000108 Liver disease due to cystic fibrosis
535011000000101 Interstitial lung disease NEC
54515008 Sarcoidosis, plaque type
54867000 Rheumatoid fibrosing alveolitis
55941000 Cutaneous sarcoidosis
56841008 Massive fibrosis of lung
57124002 Postinflammatory pulmonary fibrosis
57488007 Chronic pulmonary fibrosis due to inhalation of chemical fumes AND/OR vapors
57686001 Emphysematous bleb of lung
579661000000108 Chronic bullous emphysema NOS
58691003 Antimony pneumoconiosis
58870009 Sarcoidosis, anular type
59773008 Simple pulmonary alveolitis
598371000000106 Amyloidosis NOS
59940009 Hypersensitivity alveolitis in lungworm infection
60125001 Perinatal interstitial emphysema
6022005 Dilated cardiomyopathy secondary to sarcoidosis
604421000000104 Cystic fibrosis NOS
60805002 Hemolytic anemia with emphysema AND cutis laxa
611551000000109 Asbestosis NOS
61233003 Silo-fillers' disease
62161000000102 Interstitial lung disease annual review
62371005 Pulmonary siderosis
62382002 Calcinosis, Raynaud's phenomenon, sclerodactyly, and telangiectasia syndrome
64631008 Fullers' earth disease
64667001 Interstitial pneumonia
64757003 Lymph node sarcoidosis
649171000000104 Idiopathic fibrosing alveolitis NOS
658391000000105 Cystic fibrosis with other manifestations
66110007 Chronic diffuse emphysema caused by inhalation of chemical fumes AND/OR vapors
66987001 Congenital lobar emphysema
67242002 Bagassosis
674814021000119106 Acute respiratory distress syndrome due to disease caused by Severe acute respiratory syndrome coronavirus 2
67782005 Acute respiratory distress syndrome
68328006 Centriacinar emphysema
68333005 Furriers' lung
68759006 Idiopathic fibrosing alveolitis, subacute form
69078007 Age-related amyloidosis
69339004 Bird-fanciers' lung
697912009 Pulmonary hypertension due to interstitial lung disease
697921005 Pulmonary hypertension in sarcoidosis
697923008 Pulmonary hypertension in lymphangioleiomyomatosis
698940002 Arthropathy associated with cystic fibrosis
700249006 Idiopathic interstitial pneumonia
700250006 Idiopathic pulmonary fibrosis
700251005 Chronic idiopathic pulmonary fibrosis
700252003 Subacute idiopathic pulmonary fibrosis
703313007 Cerebral amyloid angiopathy associated with systemic amyloidosis
704345008 Chronic interstitial pneumonia
706991000000106 Arthropathy in cystic fibrosis
707001000000100 Cystic fibrosis with distal intestinal obstruction syndrome
707011000000103 Liver disease due to cystic fibrosis
707238003 Sarcoidosis of oral cavity
707418001 Male infertility due to cystic fibrosis
707419009 Osteoporosis due to cystic fibrosis
707420003 Portal hypertension due to cystic fibrosis
707433009 Lymphangioleiomyomatosis due to tuberous sclerosis syndrome
707434003 Pulmonary fibrosis due to Hermansky-Pudlak syndrome
707435002 Neuroendocrine cell hyperplasia of infancy
707442002 Congenital pulmonary alveolar proteinosis
707443007 Autoimmune pulmonary alveolar proteinosis
707450006 Pancreatic insufficiency due to cystic fibrosis of pancreas
707510005 Secondary pulmonary alveolar proteinosis
707536003 Digestive system manifestation co-occurrent and due to cystic fibrosis
707541006 Acute respiratory distress in newborn with surfactant disorder
707542004 Otorhinolaryngological manifestation co-occurrent and due to cystic fibrosis
707551007 Pulmonary interstitial glycogenosis
70756004 Bronchial atresia with segmental pulmonary emphysema
707577004 Female infertility due to cystic fibrosis
707578009 Perforation of intestine due to cystic fibrosis with meconium ileus
707734002 Elevated liver enzymes level due to cystic fibrosis
707766007 Exocrine pancreatic manifestation co-occurrent and due to cystic fibrosis
708026002 Chronic pneumonitis of infancy
708030004 Pulmonary emphysema co-occurrent with fibrosis of lung
7085002 Hypercalcemia due to sarcoidosis
708537005 Acute idiopathic pulmonary fibrosis
711379004 Interstitial lung disease due to connective tissue disease
71193007 Fibrosis of lung caused by radiation
713244007 Drug induced pulmonary fibrosis
715401008 Primary biliary cirrhosis co-occurrent with systemic scleroderma
716088000 Follicular hamartoma with alopecia and cystic fibrosis syndrome
719218000 Cryptogenic organizing pneumonia
720401009 Cystic fibrosis with gastritis and megaloblastic anemia syndrome
721197001 Polyneuropathy due to classical cystic fibrosis
721977007 Lung fibrosis, immunodeficiency, 46,XX gonadal dysgenesis syndrome
722292000 Autosomal dominant beta2-microglobulinic amyloidosis
72270005 Collagenous pneumoconiosis
722948009 Glomerular disorder due to non-neuropathic heredofamilial amyloidosis
723829000 Pulmonary fibrosis, hepatic hyperplasia, bone marrow hypoplasia syndrome
724603009 Pediatric onset systemic sclerosis
72470008 Sarcoidosis, lupus pernio type
724780002 Demyelination of central nervous system co-occurrent and due to neurosarcoidosis
724782005 Demyelination of central nervous system co-occurrent and due to Sjogren disease
725051009 Suspected cystic fibrosis in fetus
725052002 Fetal cystic fibrosis
725415009 House allergic alveolitis
73144008 Pneumoconiosis caused by talc
733422008 Prion protein systemic amyloidosis
733453005 Congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome
7343008 Liparitosis
73448002 Fish-meal workers' lung
735433009 Sarcoidosis of digestive system
737181009 Interstitial lung disease due to systemic disease
737182002 Interstitial lung disease due to granulomatous disease
737183007 Interstitial lung disease due to metabolic disease
737184001 Interstitial lung disease co-occurrent and due to systemic vasculitis
74015002 Pneumonopathy due to inhalation of dust
7436001 Alveolar pneumopathy
75403004 Cardiac sarcoidosis
7548000 Rheumatic pneumonia
76090006 Pittsburgh pneumonia
76157009 Bituminosis
762269004 Classical cystic fibrosis
762270003 Atypical cystic fibrosis
762271004 Subclinical cystic fibrosis
762303003 Pediatric onset Sjögren syndrome
770760006 16q24.1 microdeletion syndrome
771306007 Hereditary fibrosing poikiloderma, tendon contractures, myopathy, pulmonary fibrosis syndrome
774080007 Neonatal scleroderma
774082004 Neonatal dermatomyositis
77690003 Interstitial emphysema of lung
776981000000103 Cirrhosis associated with cystic fibrosis
778131000000103 Cystic fibrosis related cirrhosis
781651000000101 Respiratory bronchiolitis associated interstitial lung disease
781661000000103 Interstitial lung disease due to collagen vascular disease
781711000000106 Interstitial lung disease due to connective tissue disease
783160006 Hereditary gelsolin amyloidosis
783182004 Chronic respiratory distress with surfactant metabolism deficiency
785345002 Pneumoconiosis caused by sisal dust
78574007 Hypothyroidism due to sarcoidosis
78723001 Cannabinosis
78946008 Keratoconjunctivitis sicca, in Sjögren's syndrome
789574002 Acute exacerbation of idiopathic pulmonary fibrosis
79958002 Grain fever
805002 Pneumoconiosis caused by silica
80614003 Prolonged pulmonary alveolitis
807851000000108 Pulmonary fibrosis
807861000000106 Respiratory bronchiolitis associated interstitial lung disease
807871000000104 Interstitial lung disease due to collagen vascular disease
807891000000100 Interstitial lung disease due to connective tissue disease
80941006 Subcutaneous sarcoidosis
81423003 Cystic fibrosis without meconium ileus
817966005 Distal intestinal obstruction syndrome due to cystic fibrosis
836477007 Chronic emphysema caused by vapor
838312001 Calcinosis due to childhood type dermatomyositis
838366009 Anti-synthetase syndrome due to dermatomyositis
83901003 Sjögren's syndrome
840350008 Chronic obliterative bronchiolitis caused by chemical fumes
840351007 Chronic obliterative bronchiolitis caused by vapor
840455002 Cutaneous vasculitis due to childhood type dermatomyositis
84137001 AA amyloidosis
846637007 Chronic pulmonary fibrosis caused by chemical vapors
847091000000104 Acute non-infective exacerbation of chronic obstructive pulmonary disease
85438006 Diatomaceous earth disease
8549006 Desquamative interstitial pneumonia
855291000000104 Familial amyloid polyneuropathy type III
857271000000108 Familial amyloid polyneuropathy type II
857331000000100 Amyloid A amyloidosis
85761009 Byssinosis
85809002 Cystic fibrosis
858580008 Secondary systemic amyloidosis
859041000000103 Exacerbation of cystic fibrosis
859051000000100 Exacerbation of cystic fibrosis
860890006 Fetal interstitial neoplasm of lung
86092005 Cystic fibrosis with meconium ileus
86157004 Occupational lung disease
86263001 Cobaltosis
86365006 Poikilodermatomyositis
86555001 Cystic fibrosis of the lung
866103007 Interstitial lung disease due to juvenile polymyositis
86638007 Maple-bark strippers' lung
86680006 Ruptured emphysematous bleb of lung
870301007 Myocarditis due to childhood type dermatomyositis
870334009 Palmoplantar sarcoidosis
870336006 Necrotizing cutaneous vasculitis due to childhood type dermatomyositis
870573008 Interstitial pneumonia with autoimmune features
87153008 Pulmonary alveolar microlithiasis
87433001 Pulmonary emphysema
87442008 Pericarditis co-occurrent and due to scleroderma
875681000000100 Suspected cystic fibrosis
87909002 Hard metal pneumoconiosis
88687001 Manganese pneumonitis
89155008 Systemic sclerosis
89397007 Pulmolithiasis
89449005 Systemic amyloidosis
89681000119101 Glomerulonephritis co-occurrent and due to scleroderma
89687005 Postimmersion-submersion syndrome
90117007 Tuberculous fibrosis of lung
905381000000108 Systemic lupus erythematosus/Sjogren's overlap syndrome
90610005 Interstitial pulmonary fibrosis of prematurity
90623003 Aluminosis of lung
91259005 Sarcoidosis, angiolupoid type
9133005 Familial amyloid polyneuropathy, Iowa type
9529007 Sarcoidosis, erythrodermic type
959001000000108 Paediatric cystic fibrosis care plan
959821000000108 Adult cystic fibrosis care plan