Cystic Fibrosis

Coding system
CTV3 (Read V3)
Codelist ID

  • 2020-07-20


Codes indicating a diagnosis of cystic fibrosis or associated diseases such as primary ciliary dyskinesia


This codelist is a subset of the Chronic Respiratory Disease codelist version 2020-04-10.

This codelist was created by selecting codes relating to cystic fibrosis (not screening), fibrosing colonopathy, and primary ciliary dyskinesia. Two clinicians additionally reviewed the Chronic Respiratory Disease codelist to check for any additional codes that had been missed.


Signed off by

  • Caroline Minassian, (July 17, 2020)
  • Laurie Tomlinson, (July 18, 2020)
CTV3ID CTV3PreferredTermDesc CTV3Source
PK35. Kartageners syndrome High_Level_SNOMED
X101X Inherited mucociliary clearance defect High_Level_SNOMED
X101Z Primary ciliary dyskinesia High_Level_SNOMED
X101a Primary ciliary dyskinesia - transposn ciliary microtubules High_Level_SNOMED
X101b Immotile cilia syndrome due to defective radial spokes High_Level_SNOMED
X101c Immotile cilia syndrome due to excessively long cilia High_Level_SNOMED
X101d Young's syndrome QOF
X101e Rutland ciliary disorientation syndrome High_Level_SNOMED
C370. Cystic fibrosis CTV3Map_Code_And_Term
C370. Cystic fibrosis CTV3Map_Code_Only
C3700 Cystic fibrosis with no meconium ileus CTV3Map_Code_And_Term
C3701 Meconium ileus in cystic fibrosis CTV3Map_Code_And_Term
C3701 Meconium ileus in cystic fibrosis CTV3Map_Code_Only
C3702 Cystic fibrosis with pulmonary manifestations CTV3Map_Code_And_Term
C3703 Cystic fibrosis with intestinal manifestations CTV3Map_Code_And_Term
C370z Cystic fibrosis NOS CTV3Map_Code_And_Term
X309R Cystic fibrosis of pancreas High_Level_SNOMED
XaBDb Cystic fibrosis with other manifestations CTV3Map_Code_And_Term
XaBDb Cystic fibrosis with other manifestations CTV3Map_Code_Only
XaMzI Cystic fibrosis related diabetes mellitus QOF
XaQvd Cystic fibrosis annual review CTV3Map_Code_And_Term
XaREX Arthropathy in cystic fibrosis CTV3Map_Code_And_Term
XaREZ Cystic fibrosis with distal intestinal obstruction syndrome CTV3Map_Code_And_Term
XaREa Liver disease due to cystic fibrosis CTV3Map_Code_And_Term
XaREd Fibrosing colonopathy CTV3Map_Code_And_Term
XaXi9 Cystic fibrosis related cirrhosis CTV3Map_Code_And_Term
XaZr7 Exacerbation of cystic fibrosis CTV3Map_Code_And_Term
Y2710 Cystic fibrosis positive CTV3_Children

Codes not in the full codelist are in faint grey.