Permanent Immunosuppression

Coding system
CTV3 (Read V3)
Codelist ID

  • 2020-06-02


Codes indicating a diagnosis of a permanent immunosuppression excluding HIV, and including genetic causes of immunosuppression




Signed off by

  • Liam Smeeth, (April 24, 2020)
  • Helen McDonald, (April 23, 2020)
CTV3ID CTV3PreferredTermDesc
C390y Other specified deficiency of humoral immunity
C390z Deficiency of humoral immunity NOS
C391. Deficiencies of cell-mediated immunity
C391z Deficiency of cell-mediated immunity NOS
C393. Unspecified immunity deficiency
Cyu00 [X]Other immunodeficiencies+predominantly antibody defects
Cyu05 [X]Other specified immunodeficiency disorders
D401z Polymorphonuclear neutrophil disorder NOS
X20GZ Immunodeficiency disorder
X20HE T-lymphocyte deficiency
XaYgn Immune reconstitution syndrome
XE11u Deficiencies of humoral immunity
XE11w Predominantly T-cell immuno-deficiency NOS
C30yy (Adenosine deamin def) or (oth sp disturb amino acid metab)
C3760 C1 esterase inhibitor deficiency
C390. (Deficiencies of humoral immunity) or (agammaglobulinaemia)
C3901 Selective immunoglobulin A deficiency
C3902 Selective immunoglobulin M deficiency
C3903 Selective immunoglobulin G deficiency
C3904 Other selective immunoglobulin deficiency
C3905 Hypogammaglob:[cong][agammaglob:(Brut)(cong sex-link & [X])]
C3906 Hyperimmunoglobulin M syndrome
C3907 Common variable immunodeficiency
C3909 Agammaglobulinaemia NEC
C390A Dysimmunoglobulinaemia NEC
C3910 Cellular immunity syndr (& T-lymphocyte deficiency [& NOS])
C3911 DiGeorge syndrome
C3912 Wiskott-Aldrich syndrome
C3913 Nezelof's syndrome
C392. Combined T-cell and B-cell immunodeficiency
C3920 Autosomal recessive severe combined immunodeficiency
C3921 (Severe combined immunodefic) or (Swiss agammaglobulinaemia)
C3922 Thymic aplasia or dysplasia with immunodeficiency
C3923 Severe combined immunodefiency with reticular dysgenesis
C3924 Severe combined immunodef with low T- and B-cell numbers
C3925 Severe combined immunodef with low or normal B-cell numbers
C3928 Major histocompatibility complex class I deficiency
C3929 Major histocompatibility complex class II deficiency
C392z Combined immunity deficiency NOS
C396. Immunodef follow hereditary defect respon Epstein-Barr vir
C3980 Com var immunodef with predom abn B-cell numbers and functns
C3981 Common var immunodef predom immunoregulatory T-cell disorder
C3982 Common variable immunodef wth autoantibod to B- or T-cells
C39y0 Lymphocyte function antigen-1 defect
Cyu01 [X]Other combined immunodeficiency disorders
Cyu02 [X]Immunodeficiency associatd+other specified major defects
Cyu03 [X]Immunodeficiency associated+major defect, unspecified
Cyu04 [X]Other common variable immunodeficiencies
D2016 Pancytopenia: [with malformation]/[with pancreatitis]/[NOS]
D4001 Primary splenic neutropenia
D4005 Congenital: [neutropenia] or [agranulocytosis NEC]
D4009 Cyclical neutropenia
D401. (Funct dis polymorph neutroph)(Job's)(fam lipochr histiocyt)
D4010 Congenital dysphagocytosis
D402. (Anomaly: [genet leucocyt][epon vars]) or (Ched-Higash synd)
F14y0 Ataxia telangiectasia
M15y3 Complement 5 dysfunction
X20CO Pancytopenia with pancreatitis
X20Da Congenital agranulocytosis NEC
X20Db X-linked hypogammaglobulinaemia
X20De Chronic idiopathic neutropenia
X20Df Severe congenital neutropenia
X20Dk Myelokathexis
X20Dl Metabolic neutropenia
X20Dn Autoimmune neutropenia
X20Dv Chediak-Higashi syndrome
X20Dw Hyperimmunoglobulin E syndrome
X20Dx CR3-receptor deficiency
X20Dy Specific granule deficiency
X20E0 Chronic granulomatous disease
X20E1 Myeloperoxidase deficiency
X20E4 Hereditary hypersegmentation
X20Ga Primary immunodeficiency
X20Gb Agammaglobulinaemia
X20Gc X-linked agammaglobulinaemia
X20Gd X-linked agammaglobulinaemia with growth hormone deficiency
X20Ge Autosomal agammaglobulinaemia with absent B-cells
X20Gf Selective immunoglobulin dysfunction
X20Gg X-linked hyperimmunoglobulin M syndrome
X20Gh Autosomal recessive hyperimmunoglobulin M syndrome
X20Gj Hyperimmunoglobulin D with periodic fever
X20Gk Immunoglobulin heavy chain deficiency
X20Gn Selective immunoglobulin M and immunoglobulin A deficiency
X20Go Immunoglobulin light chain deficiency
X20Gp Kappa light chain deficiency
X20Gq Lambda light chain deficiency
X20Gr Immunoglobulin subclass deficiency
X20Gt Immunoglobulin G2 deficiency
X20Gu Combined immunoglobulin G2 and G4 deficiency
X20Gv Immunoglobulin G3 deficiency
X20Gw Immunoglobulin G4 deficiency
X20Gx Immunoglobulin G1 deficiency
X20Gy Immunoglobulin A1 deficiency
X20Gz Immunoglobulin A2 deficiency
X20H0 Immunoglobulin-associated molecule deficiency
X20H1 Secretory piece deficiency
X20H2 Defective immunoglobulin glycosylation
X20Ha Schwachman's syndrome
X20Hb Defective phagocytic cell adhesion
X20Hc Leucocyte adhesion deficiency - type 1
X20Hd Leucocyte adhesion deficiency - type 2
X20Hf Tuftsin deficiency
X20HF Chronic mucocutaneous candidiasis
X20Hg Defective phagocytic cell killing
X20HH Combined immunodeficiency with maturation pathway defect
X20HI Reticular dysgenesis
X20Hi Leucocyte glucose-6-phosphate dehydrogenase deficiency
X20HJ X-linked severe combined immunodeficiency
X20HK Severe combined immunodeficiency with short-limbed dwarfism
X20Hk Neutrophil lactoferrin deficiency
X20HL Bare lymphocyte syndrome
X20Hl Neutrophil secondary granule deficiency
X20HM Familial erythrophagocytic lymphohistiocytosis
X20Hm Gluthathione synthetase deficiency
X20HN Severe comb immunodeficiency with maternofetal engraftment
X20Hn Gluthathione peroxidase deficiency
X20HO Warts, hypogammaglobulinaemia, infections, and myelokathexis
X20Hp Combined phagocytic defect
X20Ht Classical complement pathway abnormality
X20HU Chronic familial neutropaenia
X20Hu Complement 1q deficiency
X20HV Lipochrome histiocytosis - familial
X20Hv Complement 1q beta chain deficiency
X20HW Defective phagocytic cell opsonisation
X20Hw Complement 1q dysfunction
X20HX Mannan-binding protein deficiency
X20Hx Complement 1r deficiency
X20HY Defective phagocytic cell chemotaxis
X20Hy Complement 1s deficiency
X20HZ Lazy leucocyte syndrome
X20Hz Complement 2 deficiency
X20I0 Complement 4 deficiency
X20I1 Complement 4A deficiency
X20I2 Complement 4B deficiency
X20I3 Complement 3 deficiency
X20I4 Alternative pathway deficiency
X20I5 Properdin deficiency
X20I6 Factor B deficiency
X20I7 Factor D deficiency
X20I8 Terminal component deficiency
X20I9 Complement 5 deficiency
X20Ia Chromosome 18 syndromes and antibody deficiency
X20IB Complement 6 deficiency
X20Ib Chromosome 22 abnormalities with hypogammaglobulinaemia
X20IC Complement 7 deficiency
X20Ic Monosomy 22 and absence of immunoglobulin A
X20ID Combined complement 6 and 7 deficiencies
X20Id Deletion of X-chromosome and hypogammaglobulinaemia
X20IE Complement 8 beta chain deficiency
X20Ie Microcephaly, normal intelligence and immunodeficiency
X20IF Complement 8 beta chain dysfunction
X20If Triple X syndrome, epilepsy, and hypogammaglobulinaemia
X20IG Complement 8 alpha-gamma deficiency
X20Ig 18-p syndrome with associated immunodeficiency
X20IH Complement 9 deficiency
X20Ih Immunodeficiency with multiple organ system abnormalities
X20II Complement regulatory factor defect
X20IJ Hereditary C1 esterase inhibitor defic - deficient factor
X20Ij Partial albinism with immunodeficiency
X20IK Hereditary C1 esterase inhib defic - dysfunctional factor
X20Ik X-linked lymphoproliferative syndrome
X20IL Factor I deficiency
X20IM Factor H deficiency
X20IN Complement 4 binding protein deficiency
X20IO Decay accelerating factor deficiency
X20IP Homologous restriction factor deficiency
X20IQ Complement 5a inhibitor deficiency
X20IR Anaphylotoxin inactivator deficiency
X20IS Complement receptor deficiency
X20IT Complement receptor 1 deficiency
X20IU Complement receptor 3 deficiency
X20IV Immunodeficiency with major anomalies
X20IW Immunodeficiency associated with chromosomal abnormality
X20IY Bloom syndrome
X20IZ Centromeric instability of chromosomes 1,9+16 + immunodefic
X20RX Familial chronic mucocutaneous candidiasis
X40Ua Adenosine deaminase deficiency
X40Uc Purine nucleoside phosphorylase deficiency
X70Qz Familial chronic mucocutaneous candidiasis - late onset type
X70R0 Chronic localised mucocutaneous candidiasis
X70R1 Chronic diffuse mucocutaneous candidiasis
X789w Immuno-osseous dysplasia
Xa9Az Phagocytic cell dysfunction
XaA0r Metaphys chondrodysplas, McKusick type with assoc immunodef
XE11v Congenital hypogammaglobulinaemia
XE13a Agammaglobulinaemia &/or hypo-gammaglobulinaemia
XE14B Chronic idiopathic neutropaenia
XE14F Congenital neutropenia
XE14H Functional disorders of polymorphonuclear neutrophils
8C31. Transplant immunosuppression
PK281 Congenital absence of thymus

Codes not in the full codelist are in faint grey.